Acrodermatitis Continua

Reviewed 06/2017
 


BASICS

  • Acropustular eruption with a predilection for distal digits characterized by sterile pustules; early nail involvement; and a persistent, relapsing course

  • Classified as a noninfectious neutrophil...

DIAGNOSIS

  • Defined by clinical evolution and histopathologic features

  • Frequently missed, often a diagnosis of exclusion

HISTORY

  • Onset, including any triggering event

  • Duration of eruption, previous episodes

  • ...

TREATMENT

  • Due to the rarity of this disease, only expert opinion and case reports are available to guide treatment recommendations.

  • Notoriously refractory to treatment, including topical and systemic a...

ONGOING CARE

FOLLOWUP RECOMMENDATIONS

Long-term management by a dermatologist 

PROGNOSIS

  • Generally persistent, chronically relapsing course

  • May lead to severe disability or complications warranting hospit...

REFERENCES

Lutz V, Lipsker D. Acitretin- and tumor necrosis factor inhibitor-resistant acrodermatitis continua of Hallopeau responsive to the interleukin 1 receptor antagonist anakinra. Arch Dermatol...

CODES

ICD10

L40.2 Acrodermatitis continua 

ICD9

696.1 Other psoriasis 

SNOMED

  • 200976008 Acrodermatitis continua (disorder)

  • 83839005 Acrodermatitis continua of Hallopeau

  • 58143000 Localized acrodermatitis cont...

PEARLS

  • Rare variant of pustular psoriasis that preferentially affects the fingers and toes, often leading to significant pain and loss of function

  • Classically refractory to treatment, although case rep...

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