Diffuse Interstitial Lung Disease

Reviewed 06/2018
 


BASICS

DESCRIPTION

  • Interstitial lung diseases (ILDs) represent a diverse group of chronic progressive lung diseases associated with alveolar inflammation and/or potentially irreversible pulmonary fibro...

DIAGNOSIS

  • Accurate diagnosis is imperative, as treatment choices and prognosis can vary with pathogenesis.

  • Diagnosis of IPF requires exclusion of other known ILD causes, the presence of a UIP pattern o...

TREATMENT

  • Evidence does not support the routine use of any specific therapy for ILD in general, especially IPF (2,3).

  • No survival benefit of home oxygen use in ILD

  • Corticosteroids have a role in some IL...

ONGOING CARE

FOLLOW UP RECOMMENDATIONS

Follow-up testing should include PFTs, cardiopulmonary stress test, pulse oximetry, and CXR. 

PATIENT EDUCATION

National Heart, Lung, and Blood Institute: http://ww...

REFERENCES

1 Kurland G, Deterding RR, Hagood JS, et al; for American Thoracic Society Committee on Childhood Interstitial Lung Disease (chILD) and the chILD Research Network. An official American Tho...

CODES

ICD10

  • J84.9 Interstitial pulmonary disease, unspecified

  • J84.10 Pulmonary fibrosis, unspecified

  • J84.111 Idiopathic interstitial pneumonia, not otherwise specified

  • J84.114 Acute interstitial pneumonit...

CLINICAL PEARLS

  • ILD differs from chronic obstructive pulmonary disease (COPD); anatomically, ILD involves the lung parenchyma (i.e., alveoli), and COPD involves both airways and alveoli.

  • In some cases,...

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