Bicuspid Aortic Valve Disease

Reviewed 06/2017
 


BASICS

DESCRIPTION

A bicuspid aortic valve (BAV) is an abnormal formation of the aortic valve that contains two valve leaflets instead of the usual three. This is caused by abnormal formation of the ao...

DIAGNOSIS

HISTORY

The majority of patients are asymptomatic. Some may present with symptoms associated with aortic stenosis. These symptoms may include light-headedness, syncope, chest pain, or exertio...

TREATMENT

GENERAL MEASURES

  • Patients found to have aortic diameters >4.5 cm associated with their BAV should be counseled to refrain from contact and high-intensity sports (5)[C].

  • Patients with BAV ar...

ONGOING CARE

FOLLOWUP RECOMMENDATIONS

AHA/ACC recommends that first-degree relatives be screened for BAV and aortopathy with an echocardiogram (3). 

MONITORING

  • Patients are followed with serial echocardi...

REFERENCES

Siu SC, Silversides C. Bicuspid aortic valve disease. J Am Coll Cradiol.  2010;55(25):2789–2800. [View Abstract on OvidInsights]
Mordi I, Tzemos N. Bicuspid aortic valve disease: a co...

ADDITIONAL READING

SEE ALSO

Aortic Valvular Stenosis; Aortic Regurgitation, Pediatric; Aortic Dissection 

CODES

ICD10

Q23.1 Congenital insufficiency of aortic valve 

ICD9

746.4 Congenital insufficiency of aortic valve 

SNOMED

72352009 bicuspid aortic valve (disorder) 

PEARLS

  • Patients with BAV do not need dental prophylaxis.

  • First-degree family members should receive screening for BAV via echocardiogram, CT angiography, or MRI.

  • Patients with BAV should not be restrict...

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