Behçet syndrome (BS) represents a chronic, relapsing, multisystem, autoinflammatory disorder.
Precise etiology remains incompletely understood; strong but diverse genetic component
Key symptom: Recurrent aphthous stomatitis (RAS) is the most frequent initial presenting symptom (65–70%); present in 97–100% during disease course, occurs in all three clinical subty...
Depends on severity of system involvement and medication monitoring
Periodic ophthalmologic examinations
Hamuryudan V, Hatemi G, Tascilar K, et al. Colchicine in Behçet syndrome: a longterm survey of patients in a controlled trial. J Rheumatol. 2014;41(4):735–738. [View Abstract ...
M35.2 Behcet’s disease
N77.0 Ulceration of vulva in diseases classified elsewhere
136.1 Behcet’s syndrome
616.51 Ulceration of vulva in diseases classified elsewhere
BS is a clinical diagnosis.
Consider BS in patients presenting with recurrent oral and genital ulcers.
Treatment depends on severity of disease and medication side effect profile.
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Aphthous stomatitis in Behçet's syndrome. Large, painful erosions and extensive aphthae are evident on the lips and tongue of this woman. From Goodheart HP. Goodheart's Photoguide to Common Skin Disorders: Diagnosis and Management, 3rd Edition. Philadelphia: Lippincott Williams & Wilkins, 2009.
Aphthous stomatitis in Behçet's syndrome. Large, painful erosions and extensive aphthae are evident on the lips and tongue of this woman. F...
Serpiginous ulcer of penis in patient with mouth and eye findings. Likely Behcet disease.