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Kawasaki Syndrome

Khadija Kabani, DO FAAFP and Chelsea M Shine, DO Reviewed 04/2024
 


BASICS

DESCRIPTION

  • Kawasaki syndrome (KS) is a self-limited acute, febrile, systemic vasculitis of small- and medium-sized arteries that predominantly affects patients age 6 months to 5 years

  •  The most ...

DIAGNOSIS

  • ≥5 days of fever and ≥4 of the following five principal clinical features (1); OR <4 features and presence of coronary artery disease on 2D echocardiography:

    • Bilateral, nonpurul...

TREATMENT

GENERAL MEASURES

Use antibiotics until bacterial etiologies are excluded (e.g., sepsis or meningitis). 

MEDICATION

  • Optimal therapy is IVIG 2 g/kg IV over 10 to 12 hours with high-dose aspirin p...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

With aneurysms, contact and high-risk sports should be avoided. 

Patient Monitoring

  • Repeat ECG and echocardiogram at 6 to 8 weeks. If abnormal, repeat at 6 to 12 mo...

REFERENCE

1
Son MBF, Newburger JW. Kawasaki disease. Pediatr Rev. 2018;39:78–90.

ADDITIONAL READING

  • Most ZM, Hendren N, Drazner MH, et al. The striking similarities of multisystem inflammatory syndrome in children and a myocarditis-like syndrome in adults: overlapping m...

CODES

ICD10

M30.3 Mucocutaneous lymph node syndrome [Kawasaki] 

SNOMED

75053002 Acute febrile mucocutaneous lymph node syndrome (disorder) 

CLINICAL PEARLS

  • The diagnosis of KS rests on a constellation of clinical features.

  • Once KS is suspected, all patients need an inpatient cardiac evaluation, including ECG and echocardiogram.

  • Optimal ther...

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