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Polyarteritis Nodosa

Ratnesh Chopra, M.D. and Yevgeniy Popov, MPH, D.O Reviewed 05/2023
 


BASICS

DESCRIPTION

  • Polyarteritis nodosa (PAN) is an antineutrophil cytoplasmic antibody (ANCA)-negative necrotizing arteritis of medium-sized muscular arteries and (occasionally) small arteries. Arteri...

DIAGNOSIS

  • There are no formal diagnostic criteria for PAN (2).

  • Suspect PAN with:

    • Acute, sometimes fulminant multisystem disease with a relatively short prodrome (i.e., weeks to months).Vasculitic skin ...

TREATMENT

GENERAL MEASURES

Treat HTN aggressively to prevent complications (stroke, myocardial infarction, heart failure). 

MEDICATION

First Line

  • Severe (life-threatening) disease: corticosteroids (CS) (h...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

  • For patients with severe abdominal disease who become asymptomatic, follow up vascular imaging is recommended (1).

  • For patients with peripheral motor neuropathy s...

REFERENCES

1
Chung SA, Langford CA, Maz M, et al. 2021 American College of Rheumatology/Vasculitis Foundation Guideline for the Management of Polyarteritis Nodosa. Arthritis Rheumatol. 2021;73(8):1384-...

SEE ALSO

Hepatitis B; Hepatitis C 

CODES

ICD10

  • M30.0 Polyarteritis nodosa

  • M30.1 Polyarteritis with lung involvement [Churg-Strauss]

  • M30.8 Other conditions related to polyarteritis nodosa

  • M31.7 Microscopic polyangiitis

SNOMED

  • 155441006 Polyar...

CLINICAL PEARLS

  • PAN is a necrotizing vasculitis of small- to medium-sized muscular arteries with lack of granuloma formation that spares veins and pulmonary arteries.

  • Clinical features of PAN depend on...

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