Pulmonary alveolar proteinosis (PAP) is a rare disease characterized by accumulation of lipoproteinaceous (surfactant-like) material in the alveolar spaces, leading to impaired gas e...
Diagnosis often delayed due to nonspecific presentation
Occupational and exposure history to exclude secondary PAP
Symptoms
Progressive dyspnea with insidious onset (most common presenta...
Supportive measures such as supplemental oxygen, bronchodilators, and antibiotics for infection, smoking cessation, and treatment of concurrent diseases that impair respirato...
Beccaria M, Luisetti M, Rodi G, et al. Long-term durable benefit after whole lung lavage in pulmonary alveolar proteinosis. Eur Respir J. 2004;23(4):526–531.
Chung MJ, Lee KS, ...
PAP is a rare disease characterized by accumulation of PAS-positive surfactant-like material in the alveolar spaces leading to impaired gas exchange.
Nonspecific respiratory symptoms an...
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