Pulmonary alveolar proteinosis (PAP) or pulmonary alveolar phospholipoproteinosis, first described in 1958 by Rosen et al, is characterized by overproduction of abnormal, nonfunction...
Diagnosis often delayed due to nonspecific presentation, therefore, high clinical suspicion with thorough occupational and exposure history should be obtained (2)
Clinical manifestati...
Management is based on disease progression, coexisting infections, and degree of physiologic impairment (5,6).
In general, patient is classified as asymptomatic or symptomatic. The latter mi...
European Management Platform: www.childeu.net www.childeu.net ??[View Abstract on OvidMedline]
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PAP is a rare disease characterized by accumulation of PAS-positive surfactant-like material in the alveolar spaces leading to impaired gas exchange.
Nonspecific respiratory symptoms an...
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