Pulmonary fibrosis (PF) is a part of interstitial lung diseases (ILDs) that is a family of >200 different lung diseases, which are characterized by inflammation, cellular prolifer...
Very insidious and slow onset
Exertional breathlessness and nonproductive cough
Constitutional symptoms are uncommon but can present with weight loss, fever, fatigue, myalgias, and arth...
Referral to a transplant center
Clinical practice guidelines strongly recommend supplemental oxygen.
Pulmonary clinic and, if possible, at an ILD clinic.
Monitoring with serial HRCT and PFT along with 6MWD and exercise oximetry
If on treatment with any of the newly...
J84.10 Pulmonary fibrosis, unspecified
J84.112 Idiopathic pulmonary fibrosis
515 Postinflammatory pulmonary fibrosis
516.31 Idiopathic pulmonary fibrosis
51615001 Fibrosis of lung (di...
IPF is most common idiopathic ILD and frequently misdiagnosed and mistreated.
High Resolution CT scan is the cornerstone for diagnosis.
Until recently available two newer drugs, no other...
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