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Pulmonary Valve Stenosis

Reviewed 06/2018
 


BASICS

DESCRIPTION

Deformity of pulmonary valve, resulting in obstruction of right ventricular (RV) outflow 

EPIDEMIOLOGY

Incidence

  • Predominant age: congenital, present in newborns but often asymptomatic ...

DIAGNOSIS

HISTORY

  • History of heart murmur since birth

  • Usually asymptomatic (mild to moderate stenosis); exercise tolerance is normal unless stenosis is severe.

  • If critical stenosis may have feeding intol...

TREATMENT

Described in “Surgery/Other Procedures” 

GENERAL MEASURES

Prophylaxis for subacute bacterial endocarditis is not recommended for pulmonary valve stenosis unless the patient has associated cong...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

The American College of Cardiology and the American Heart Association recommend that (2)[C]: 
  • For valvular stenosis:

    • Asymptomatic patients with a peak instantaneous...

REFERENCES

1
Nembhard WN, Wang T, Loscalzo ML, et al. Variation in the prevalence of congenital heart defects by maternal race/ethnicity and infant sex. J Pediatr.  2010;156(2):259–264. [View Abst...

ADDITIONAL READING

  • Harrild DM, Powell AJ, Tran TX, et al. Long-term pulmonary regurgitation following balloon valvuloplasty for pulmonary stenosis risk factors and relationship to exercise capacity an...

SEE ALSO

Noonan Syndrome with Multiple Lentigines (LEOPARD Syndrome); Tetralogy of Fallot; Williams-Beuren Syndrome 

CODES

ICD10

  • Q22.1 Congenital pulmonary valve stenosis

  • I37.0 Nonrheumatic pulmonary valve stenosis

  • I09.89 Other specified rheumatic heart diseases

  • T82.857A Stenosis of cardiac prosthetic devices, implants ...

CLINICAL PEARLS

  • Pulmonary stenosis is a common congenital condition that can be isolated or a part of other syndromes.

  • The most common cause is congenital rubella infection.

  • Vaccinating the population (...

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