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Rhabdomyosarcoma

Vincent L Shaw, Jr, CAQ-SM, MD Reviewed 06/2022
 


BASICS

DESCRIPTION

Rhabdomyosarcoma (RMS) is a malignant tumor of soft tissue assumed to originate from the same pluripotent mesenchyme cell as striated skeletal muscle. It occurs mainly as primary mal...

DIAGNOSIS

HISTORY

  • Presents as a progressive non-tender palpable mass

  • When presents in the head/neck, patients report diplopia (due to ophthalmoplegia), recurrent sinusitis, or persistent nasal discharge...

TREATMENT

Encompasses surgical resection, radiation, chemotherapy. Patients should always be referred to a multidisciplinary team with expertise in oncology for definitive treatment. 

SURGERY/OTHER PROCEDURES

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

All patients should follow up with their multidisciplinary team. This allows monitoring of treatment response, early detection of locoregional relapse, metastatic...

REFERENCES

1
PDQ Pediatric Treatment Editorial Board. Childhood Rhabdomyosarcoma Treatment (PDQ®): Health Professional Version. 2021 Sep 23. In: PDQ Cancer Information Summaries [Internet]. Bethesda (M...

CODES

ICD10

  • C49.9 Malignant neoplasm of connective and soft tissue, unsp

  • C49.0 Malignant neoplasm of connective and soft tissue of head, face and neck

  • C49.5 Malignant neoplasm of connective and soft tiss...

CLINICAL PEARLS

  • RMS is more common in children but can develop in adults, the latest having the highest mortality.

  • Genetic disorders and congenital syndromes are associated with a higher risk of develo...

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