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Rhabdomyosarcoma

Reviewed 06/2019
 


BASICS

DESCRIPTION

Rhabdomyosarcoma (RMS) is a malignancy which form part from soft tissue tumors named sarcomas. RMS generates from primitive mesenchymal cells with myogenesis capacity, which matures ...

DIAGNOSIS

HISTORY

  • Presents as a progressive nontender palpable mass

  • When presents in head/neck, patients report diplopia (due to ophthalmoplegia), recurrent sinusitis, or persistent nasal discharge.

  • RMS ...

TREATMENT

Encompasses surgical resection, radiation, chemotherapy. Patients should always be referred to a multidisciplinary team with expertise in oncology for definitive treatment. 

SURGERY/OTHER PROCEDURES

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

All patients should follow-up with their multidisciplinary team. This allows to monitor treatment response, early detection of locoregional relapse, metastatic di...

REFERENCES

1
Khosla D, Sapkota S, Kapoor R, et al. Adult rhabdomyosarcoma: clinical presentation, treatment, and outcome. J Cancer Res Ther.  2015;11(4):830–834. [View Abstract on OvidMedline]
2
Nat...

CODES

ICD10

  • C49.9 Malignant neoplasm of connective and soft tissue, unsp

  • C49.0 Malignant neoplasm of connective and soft tissue of head, face and neck

  • C49.5 Malignant neoplasm of connective and soft tiss...

CLINICAL PEARLS

  • RMS are more common in children but can develop in adults, the latest having the highest mortality.

  • Genetic disorders and congenital syndromes are associated to a higher risk of develop...

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