A group of inherited hematologic disorders that affect the synthesis of adult hemoglobin tetramer (HbA) (1)
α-Thalassemia is due to a deficient synthesis of α-globin chain, whereas β...
Poor growth
Excessive fatigue
Cholelithiasis
Pathologic fractures
Shortness of breath
Pallor
Splenomegaly
Jaundice
Maxillary hyperplasia/frontal bossing due to massive bone marro...
Outpatient for mild cases
Inpatient for transfusion therapy
Mild cases (trait or minor) require no therapy.
Thalassemia intermedia: No therapy is necessary unless hemoglobin fal...
Thalassemia trait requires no restrictions.
β-Thalassemia major
Avoid strenuous activities (e.g., football, soccer).
Acceptable activity levels will be determined on...
D56.5 Hemoglobin E-beta thalassemia
D56.3 Thalassemia minor
D56.0 Alpha thalassemia
D56.4 Hereditary persistence of fetal hemoglobin [HPFH]
D56.8 Other thalassemias
D56.2 Delta-beta thalassemia
D...
Thalassemia (group of inherited hematologic disorders that affect the synthesis of adult hemoglobin tetramer) is a genetic condition; hemoglobin will not improve over time.
α-Thalassemi...
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