Skip to main content

Vasculitis

Irene J. Tan, FACR, MD Reviewed 05/2023
 


BASICS

DESCRIPTION

An inflammatory disorder of blood vessels 
  • Clinical features result from the destruction of blood vessel walls with subsequent thrombosis, ischemia, bleeding, and/or aneurysm formatio...

DIAGNOSIS

HISTORY

  • Consider age, gender, and ethnicity.

  • Comprehensive medication history

  • Family history of vasculitis

  • Constitutional symptoms: fever, weight loss, malaise, fatigue, diminished appetite, swe...

TREATMENT

GENERAL MEASURES

  • Discontinue offending drug (hypersensitivity vasculitis).

  • Simple observation for mild cases of pediatric IgA vasculitis

  • ANCA-associated vasculitis has two-phase treatment: init...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

If significant coronary artery disease is involved in KD, moderate activity restriction may be of benefit. 

Patient Monitoring

Frequent clinical follow-up supported...

REFERENCES

1
Sunderkotter CH, Zelger B, Chen KR, et al. Nomenclature of cutaneous vasculitis: Dermatologic addendum to the 2012 Revised International Chapel Hill Consensus Conference nomenclature of va...

ADDITIONAL READING

  • Iba T, Connors JM, Levy JH. The coagulopathy, endotheliopathy, and vasculitis of COVID-19. Inflamm Res. 2020;69(12):1181-1189

  • Walsh M, Merkel PA, Peh ...

CODES

ICD10

  • M31.7 Microscopic polyangiitis

  • M31.30 Wegener's granulomatosis without renal involvement

  • M31.9 Necrotizing vasculopathy, unspecified

  • M30.0 Polyarteritis nodosa

  • M31.2 Lethal midline granuloma

  • M31...

CLINICAL PEARLS

  • Suspect vasculitis in patients with a petechial rash, palpable purpura, glomerulonephritis, pulmonary-renal syndrome, intestinal ischemia, or mononeuritis multiplex.

  • Exclude silent rena...

Subscribe to Access Full Content

Sign Up for a 10-Day Free Trial

Sign up for a 10-day FREE Trial now and receive full access to all content.

 
×