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von Willebrand Disease

Diana Desai, MD, MBA Reviewed 06/2020
 


BASICS

DESCRIPTION

  • von Willebrand disease (vWD) is an inherited bleeding disorder resulting from either a quantitative or qualitative defect in von Willebrand factor (vWF) protein.

  • vWF plays an essentia...

DIAGNOSIS

HISTORY

  • Most patients with vWD have a positive family history of a bleeding disorder; however, patients with mild forms of vWD and their families may be unaware of their disease. Those with A...

TREATMENT

GENERAL MEASURES

  • Minor bleeding episodes generally do not require therapeutic intervention. Most commonly, these individuals receive treatment prior to receiving surgeries, dental procedures,...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

Patients should be seen by a hematologist prior to invasive procedures. 

Patient Monitoring

Patients with mild disease do not require monitoring. 

DIET

No dietary res...

REFERENCES

1
Baronciani L, Peyvandi F. How we make an accurate diagnosis of von Willebrand disease [published online ahead of print July 16, 2019]. Thromb Res. doi: 10.1016/j.thromres.2019.07.010.

ADDITIONAL READING

SEE ALSO

Algorithms: Bleeding Gums; Ecchymosis 

CODES

ICD10

D68.0 Von Willebrand’s disease 

ICD9

286.4 Von Willebrand’s disease 

SNOMED

  • 128105004 von Willebrand disorder (disorder)

  • 128106003 von Willebrand disease type 1 (disorder)

  • 128107007 von Willebran...

CLINICAL PEARLS

  • vWD is the most common inherited bleeding disorder in American women, and its manifestations vary from minor to severe bleeding episodes.

  • Treatment should be administered for recurrent ...

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