Most common presenting respiratory symptoms: chronic cough, recurrent pneumonia, nasal polyps, chronic pansinusitis
Most common presenting GI symptoms:
Meconium ileus (15–20% of patient...
Antibiotic therapy based on sputum culture results and clinical improvement:
Oral antibiotics:
Cephalexin
Linezolid
Trimethoprim-sulfamethoxazole
Doxycycline
Ciprofloxacin
Inhal...
Newborns should be seen in a CF center within 48 to 72 hours after a diagnosis has been established.
In infants with positive newborn screen...
Baumer JH. Evidence based guidelines for the performance of the sweat test for the investigation of cystic fibrosis in the UK. Arch Dis Child. 2003;88(12):1126–1127. [View Abs...
277.00 Cystic fibrosis without mention of meconium ileus
277.02 Cystic fibrosis with pulmonary manifestations
277.01 Cystic fibrosis with meconium ileus
277.03 Cystic fibrosis with gastrointest...
Q: Should relatives be tested?
A: All siblings should have a sweat test.
Q: How well will a child with CF do?
A: The course of the illness is variable. It is difficult to predict the course of diseas...
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