Congenital motor disorder of the gut characterized by lack of ganglion cells in the distal bowel beginning at the anal verge and extending proximally to varying lengths
Lack of intern...
80% of patients present in the neonatal period.
15% diagnosed in 1st month, 40–50% within 3 months, 60% within 1 year, and 85% within 4 years
Adult diagnosis of HD reported in 2% of pop...
Followed on a regular basis for the 1st decade after surgery
Close monitoring for poor growth, fecal incontinence, obstructive symptoms (constipation, abdominal di...
Chumpitazi B, Nurko S. Defecation disorders in children after surgery for Hirschsprung disease. J Pediatr Gastroenterol Nutr. 2011;53(1):75–79. [View Abstract on OvidInsights]
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751.3 Hirschsprung’s disease and other congenital functional disorders of colon
Q43.1 Hirschsprung’s disease
204739008 Hirschsprung’s disease (disorder)
204745000 Total intestinal ag...
Q: What is the likelihood that a newborn with a diagnosis of HD will have normal bowel function after surgery?
A: There is a good likelihood, but it may take a number of years: A review of 178 pati...
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