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Hypogammaglobulinemia, Pediatric

Rachel G. Robison, MD Reviewed 10/2018
 


BASICS

DESCRIPTION

  • A disorder of the humoral immune system characterized by deficient or absent immunoglobulins and the inability to produce specific antibody

  • Subtypes include primary immunodeficiency a...

DIAGNOSIS

HISTORY

  • Recurrent upper and lower respiratory tract infections (otitis media, pneumonia, and sinusitis)

  • Infections with encapsulated bacteria such as Streptococcus pneumoniae, Haemophilus infl...

TREATMENT

MEDICATION

  • Appropriate antimicrobial therapy at first sign of infection. Prompt initiation of therapy is recommended.

  • Select patients may benefit from prophylactic antibiotics.

  • Regular replacem...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

Patient Monitoring

Patients on immunoglobulin replacement should have trough IgG levels followed regularly as well as CBCs with differential and metabolic panels t...

ADDITIONAL READING

  • Conley ME. Genetics of hypogammaglobulinemia: what do we really know? Curr Opin Immunol.  2009;21(5):466–471. [View Abstract on OvidInsights]

  • Jolles S. The variable in common va...

CODES

ICD9

  • 279.00 Hypogammaglobulinemia, unspecified

  • 279.04 Congenital hypogammaglobulinemia

  • 279.01 Selective IgA immunodeficiency

  • 279.02 Selective IgM immunodeficiency

  • 279.03 Other selective immunoglobuli...

FAQ

  • Q: When should I check immunoglobulin levels?

  • A: Immunoglobulins and antibody responses to vaccinations may be considered in any patient with a history of recurrent sinopulmonary infections.

  • Q: I ha...

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