In the current era, HLHS is often diagnosed prenatally.
Postnatal signs and symptoms:
Respiratory distress (tachypnea, grunting, flaring, retractions)
Cyanosis
Cardiovascular collapse and...
Initial stabilization
During initial resuscitation and stabilization of a newly diagnosed infant:
Prostaglandin E1 therapy should be initiated as soon as possible to maintain ductal patency.
Av...
Alsoufi B, Bennetts J, Verma S, et al. New developments in the treatment of hypoplastic left heart syndrome. Pediatrics. 2007;119(1):109–117. [View Abstract on OvidInsights]
Gr...
746.7 Hypoplastic left heart syndrome
758.6 Gonadal dysgenesis
759.89 Other specified congenital anomalies
Q24.8 Other specified congenital malformations of heart
Q96.9 Turner’s syndrome, u...
Q: What is the significance of an intact or restrictive atrial septum during the initial stabilization of a neonate with HLHS?
A: In HLHS patients, restriction to left-to-right flow across the atri...
Sign up for a 10-day FREE Trial now and receive full access to all content.
<bold>Figure 33-30</bold> Electrocardiogram shows low left precordial forces in a cyanotic newborn with hypoplastic left heart syndrome.
<bold>Figure 33-30</bold> Electrocardiogram shows low left precordial forces in a cyanotic newborn with hypoplastic left heart...
<bold>Figure 33-31</bold> Echocardiographic parasternal long-axis view in an infant with hypoplastic left heart syndrome. The right ventricle (RV) is near normal in size. The left atrium (LA), left ventricle (LV) and ascending aorta (AO) are tiny. Both the mitral and aortic valves are atretic.
<bold>Figure 33-31</bold> Echocardiographic parasternal long-axis view in an infant with hypoplastic left heart syndrome. The ...
<bold>Fig CA 1-3 Hypoplastic left heart syndrome.</bold> Globular cardiomegaly with severe pulmonary venous congestion.
<bold>Fig CA 8-4 Hypoplastic left heart syndrome.</bold> Globular cardiomegaly with pronounced congestive failure.
A case of complex congenital heart disease. Patient has situs inversus, dextrocardia, is status-post tetralogy of Fallot repair, and presents with symptoms of right-sided heart failure. A: Axial gradient echo images showing dextrocardia and right ventricular dilation. B: Sagittal gradient-echo images showing free pulmonary regurgitation (arrow) at the site of previous infundibular resection.
A case of complex congenital heart disease. Patient has situs inversus, dextrocardia, is status-post tetralogy of Fallot repair, and prese...