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Imperforate Anus, Pediatric

Lusine Ambartsumyan, MD Reviewed 10/2018
 


BASICS

DESCRIPTION

  • Imperforate anus (IA) is a congenital abnormality in which the bowel fails to perforate or only partially perforates the pelvic muscular floor.

  • IA may also perforate the epidermal cov...

DIAGNOSIS

HISTORY

  • May be diagnosed prenatally (dilated colon, oligohydramnios) especially in setting of associated anomalies

  • Most children are diagnosed during a routine neonatal examination.

  • Failure to ...

TREATMENT

SURGERY/OTHER PROCEDURES

  • Surgery should be performed by an experienced surgeon.

  • High lesions require an emergent and protective diverting colostomy, followed by pull-through procedure with pos...

ONGOING CARE

PATIENT EDUCATION

  • Prognosis for bowel and urine continence depends on the type of anorectal malformation, degree of associated defects, presence of spinal abnormalities, and sacral integri...

ADDITIONAL READING

  • Bischoff A, Levitt MA, Peña A. Update on the management of anorectal malformations. Pediatr Surg Int.  2013;29(9):899–904. [View Abstract on OvidInsights]

  • Bischoff A, Martinez-L...

CODES

ICD9

  • 751.2 Atresia and stenosis of large intestine, rectum, and anal canal

  • 565.1 Anal fistula

ICD10

  • Q42.3 Congenital absence, atresia and stenosis of anus without fistula

  • Q42.2 Congenital absence, at...

FAQ

  • Q: Is IA an isolated defect in my child?

  • A: IA is often associated with multiple other anomalies. In particular, renal and vertebral anomalies must be excluded.

  • Q: What is the genetic basis for this...

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