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Tracheoesophageal Fistula and Esophageal Atresia, Pediatric

Reviewed 10/2018
 


BASICS

DESCRIPTION

  • Esophageal atresia with tracheoesophageal fistula (EA-TEF) is a congenital condition of incomplete formation of the esophagus. In most cases, the atretic (blind-ending) esophagus has...

DIAGNOSIS

HISTORY

  • Prenatal ultrasound may demonstrate features suggestive of EA-TEF such as absence of a stomach bubble, a dilated proximal pouch, or polyhydramnios.

    • Only a minority of patients are pren...

TREATMENT

GENERAL MEASURES

Preoperative management 
  • Strict NPO until surgical correction is undertaken

  • Maintain a Replogle suction tube in the proximal pouch to decrease aspiration from pooled secretions...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

  • EA-TEF patients require long-term follow-up for GERD, dysphagia, and esophageal motility issues.

  • Surveillance endoscopy may be considered in young adulthood for ri...

ADDITIONAL READING

  • Burge DM, Shah K, Spark P, et al; for British Association of Paediatric Surgeons Congenital Anomalies Surveillance System. Contemporary management and outcomes for infants born with...

CODES

ICD9

  • 750.3 Tracheoesophageal fistula, esophageal atresia and stenosis

  • 748.3 Other anomalies of larynx, trachea, and bronchus

ICD10

  • Q39.1 Atresia of esophagus with tracheoesophageal fistula

  • Q39.2 Cong...

FAQ

  • Q: What is the diagnostic workup for suspected TEF?

  • A: A chest radiograph with gentle forward pressure held on the nasogastric tube is the preferred diagnostic study. Without pressure, the film may...

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