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Von Willebrand Disease, Pediatric

Char M. Witmer, MD, MSCE Reviewed 10/2018
 


BASICS

DESCRIPTION

  • An inherited bleeding disorder caused by either a quantitative or qualitative defect of the von Willebrand protein

  • Characterized by mucocutaneous bleeding or bleeding after surgical p...

DIAGNOSIS

HISTORY

  • A family history of von Willebrand disease or bleeding tendency is an important question in the evaluation for von Willebrand disease. However, be aware that variation in frequency an...

TREATMENT

GENERAL MEASURES

  • There are several options for the management of bleeding in patients with von Willebrand disease. Superficial bleeding can usually be stopped by applying local pressure, ice,...

ONGOING CARE

PROGNOSIS

  • von Willebrand disease type 1 is often a very mild bleeding disorder and may go undetected.

  • Most patients with von Willebrand disease have a normal life expectancy and, with prope...

ADDITIONAL READING

  • Cox Gill J. Diagnosis and treatment of von Willebrand disease. Hematol Oncol Clin North Am.  2004;18(6):1277–1299. [View Abstract on OvidInsights]

  • Mannucci PM. Treatment of von ...

CODES

ICD9

286.4 Von Willebrand’s disease 

ICD10

D68.0 Von Willebrand’s disease 

SNOMED

  • 128105004 von Willebrand disorder (disorder)

  • 128106003 von Willebrand disease type 1 (disorder)

  • 128107007 von Willebran...

FAQ

  • Q: What sports activities can a person with von Willebrand disease participate in safely?

  • A: People with type 1 von Willebrand disease can participate in most activities, although it is usually adv...

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