Skip to main content

Wilms Tumor, Pediatric

Nicholas F. Evageliou, MD Reviewed 10/2018
 


BASICS

DESCRIPTION

Wilms tumor is a malignant tumor of the kidney occurring in the pediatric age group. It is also referred to as nephroblastoma. 

EPIDEMIOLOGY

Slightly more common in girls than boys; 90...

DIAGNOSIS

HISTORY

  • Abdominal distention, most often painless

  • Abdominal pain (20–30% of cases)

  • Hematuria (20–30% of cases)

  • Fever, anorexia, vomiting

  • Family history of Wilms tumor

  • Rapid increase in abdominal s...

TREATMENT

Radiotherapy 
  • Not required for stage I and II patients unless anaplastic, clear cell, or rhabdoid

  • Radiotherapy to tumor bed with 1,080 cGy for stages III and IV; if gross tumor spillage or per...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

Patient Monitoring

  • Every 3 months for 18 months, every 6 months for 1 year, and then yearly

  • Chest radiograph, urinalysis, and abdominal ultrasound at regular interv...

ADDITIONAL READING

  • Davidoff AM, Wilms tumor. Adv Pediatr.  2012;59(1):247–267. [View Abstract on OvidInsights]

  • Dome JS, Graf N, Geller JI, et al. Advances in Wilms tumor treatment and biology: pro...

CODES

ICD9

189.0 Malignant neoplasm of kidney, except pelvis 

ICD10

  • C64.9 Malignant neoplasm of unsp kidney, except renal pelvis

  • C64.1 Malignant neoplasm of right kidney, except renal pelvis

  • C64.2 Malignan...

FAQ

  • Q: Can a child grow and live normally with one kidney?

  • A: Yes. Studies of children with unilateral nephrectomy show a rate of chronic renal failure at 25 years of <1%.

  • Q: What is my child’s risk ...

Subscribe to Access Full Content

Sign Up for a 10-Day Free Trial

Sign up for a 10-day FREE Trial now and receive full access to all content.

 
×