Described in 1886 by Harold Hirschsprung as a cause of constipation in early infancy
Congenital aganglionosis megacolon
1:5,000 live births
Overall mortality of Hirschsprung enterocolit...
Three presentations, varying with age:
Failure of passage of meconium...
Airway, breathing, and circulation management with monitoring as appropriate
Initial bolus of isotonic IV fluids (20 cc/kg) for shock, dehydration, sepsis
Neonates and infants presenting with bowel obstruction
Ill-appearing infants should be admitted to a neonatal/pediatric intensive care unit with avai...
Presentation varies with the age of the child
Continuum may vary from toxicity and enterocolitis to chronic constipation
Toxic child need stabilization, antibiotics and emergent imag...
Amiel J, Lyonnet S. Hirschsprung disease, associated syndromes, and genetics: A review. J Med Genet. 2001;38:729–739.
Kays DW. Surgical conditions of the neonatal intestinal...
204739008 Hirschsprung's disease (disorder)
204741009 Short segment Hir...
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