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Multicystic Dysplastic Kidney, Pediatric

Kelly A. Benedict, MD Reviewed 10/2018
 


BASICS

DESCRIPTION

  • Multicystic dysplastic kidney (MCDK) disease is the most severe type of cystic renal dysplasia and is characterized by multiple, noncommunicating cysts which are divided by dysplasti...

DIAGNOSIS

HISTORY

  • Commonly diagnosed by antenatal ultrasound

  • May present as abdominal or flank mass

PHYSICAL EXAM

  • Blood pressure at each visit to monitor for hypertension

  • Evaluate height and weight.

  • Neonate...

TREATMENT

GENERAL MEASURES

  • No specific treatment is needed for MCDK.

  • Previously, nephrectomy was treatment of choice; however, given low risk of hypertension and malignancy, currently, routine nephrecto...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

  • Blood pressure monitoring

    • Anecdotally, these patients were thought to be at risk for hypertension.

    • However, more recent studies show no increased risk.

  • Patients may ...

ADDITIONAL READING

  • Aslam M, Watson AR; for Trent & Anglia MCDK Study Group. Unilateral multicystic dysplastic kidney: long term outcomes. Arch Dis Child.  2006;91(10):820–823. [View Abstract ...

CODES

ICD9

  • 753.15 Renal dysplasia

  • 753.12 Polycystic kidney, unspecified type

ICD10

  • Q61.4 Renal dysplasia

  • Q61.3 Polycystic kidney, unspecified

SNOMED

  • 204949001 Renal dysplasia (disorder)

  • 82525005 Congenital cy...

FAQ

  • Q: What can be done to preserve contralateral renal function?

  • A: Well-controlled blood pressure, treatment of proteinuria, and quick treatment of UTI may decrease the progression of CKD.

  • Q: Are pati...

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