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Restrictive Cardiomyopathy

Inderjit Singh, MD and Saahil A Jumkhawala, MBA, MD Reviewed 05/2023
 


BASICS

DESCRIPTION

  • Restrictive cardiomyopathy (RCM) represents a heterogeneous group of myocardial diseases characterized by decreased left ventricular compliance, leading to an increase in end-diastol...

DIAGNOSIS

HISTORY

  • Patients typically present with symptoms of heart failure including dyspnea, orthopnea, paroxysmal nocturnal dyspnea (PND), ascites, lower extremity swelling, generalized weakness, an...

TREATMENT

GENERAL MEASURES

  • RCM treatment is aimed at lowering left ventricular filling pressures without affecting cardiac output adversely.

  • Therapeutic modalities aimed at treating the underlying cause...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

Close follow-up after hospital discharge with aims to reduce readmission 

Patient Monitoring

  • Change in degree of dyspnea or NYHA class

  • Edema, ascites

  • Daily weights

DIET

REFERENCES

1
Gupta  A, Singh Gulati  G, Seth  S, et al. Cardiac MRI in restrictive cardiomyopathy. Clin Radiol.  2012;67(2):95–105. [View Abstract on OvidMedline] ...

ADDITIONAL READING

Towbin  JA. Inherited cardiomyopathies. Circ J.  2014;78(10):2347–2356. [View Abstract on OvidMedline]  

CODES

ICD10

  • I42.5 Other restrictive cardiomyopathy

SNOMED

  • 415295002 Restrictive cardiomyopathy

  • 90828009 Primary restrictive cardiomyopathy

  • 415509000 Secondary restrictive cardiomyopathy

  • 233878008 Familial r...

CLINICAL PEARLS

  • Maintain high index of suspicion to diagnose RCM, especially in cases of recurrent heart failure decompensation. The most common cause of RCM is cardiac amyloidosis; increased wall thi...

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