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Restrictive Cardiomyopathy

Reviewed 06/2019
 


BASICS

DESCRIPTION

  • Restrictive cardiomyopathy (RCM) is a heterogeneous group of myocardial diseases characterized by decreased left ventricular compliance, leading to an increase in end-diastolic filli...

DIAGNOSIS

HISTORY

  • Patients typically present with symptoms of heart failure including dyspnea, orthopnea, paroxysmal nocturnal dyspnea (PND), ascites, lower extremity swelling, generalized weakness, an...

TREATMENT

GENERAL MEASURES

  • RCM treatment is aimed at lowering left ventricular filling pressures without affecting cardiac output adversely.

  • Therapeutic modalities aimed at treating the underlying cause...

ONGOING CARE

FOLLOW-UP RECOMMENDATIONS

Close follow-up after hospital discharge with aims to reduce readmission 

Patient Monitoring

  • Change in degree of dyspnea or NYHA class

  • Edema, ascites

  • Daily weights

DIET

REFERENCES

1
Gupta A, Singh Gulati G, Seth S, et al. Cardiac MRI in restrictive cardiomyopathy. Clin Radiol.  2012;67(2):95–105. [View Abstract on OvidMedline]
2
Cooper LT, Baughman KL, Feldman AM, ...

ADDITIONAL READING

  • Artz G, Wynne J. Restrictive cardiomyopathy. Curr Treat Options Cardiovasc Med.  2000;2(5):431–438. [View Abstract on OvidMedline]

  • Towbin JA. Inherited cardiomyopathies. Circ J....

CODES

ICD10

I42.5 Other restrictive cardiomyopathy 

ICD9

425.4 Other primary cardiomyopathies 

SNOMED

  • 415295002 Restrictive cardiomyopathy (disorder)

  • 79754008 Restrictive cardiomyopathy secondary to amyloid...

CLINICAL PEARLS

  • Maintain high index of suspicion to diagnose RCM, especially in cases of recurrent heart failure decompensation. The most common cause of RCM is cardiac amyloidosis; increased wall thi...

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