Systemic sclerosis (SSc) is an autoimmune vasculopathic disease causing fibrosis of skin and internal organs.
SSc is a type of scleroderma (meaning “hard skin”) but should not be conf...
Onset is almost always insidious.
Initial symptoms in SSc
Reflection of vasculopathy in microvasculature
Nailfold capillary changes and distorted/thickened cuticles
Collaborative care with subspecialists (pulmonary, GI, cardiology), school, social work, physical therapy
Supportive care: Avoid skin trauma; wound care for digital and other ...
Physical exam for digital or other skin ulcerations, joint mobility, muscle bulk, weight loss, poor growth
Pulmonary function tests and echocardi...
Foeldvari I. Update on juvenile systemic sclerosis. Curr Opin Rheumatol. 2015;17(3):18. [View Abstract on OvidInsights]
Martini G, Foeldvari I, Russo R, et al; for Juvenile Scl...
M34.9 Systemic sclerosis, unspecified
M34.89 Other systemic sclerosis
128461001 Systemic sclerosis sine scleroderma
89155008 Systemic sclerosis
Sign up for a 10-day FREE Trial now and receive full access to all content.