Hemophagocytic lymphohistiocytosis (HLH) is a rare clinical syndrome characterized by excessive activation of the immune system resulting in over production of inflammatory cytokines...
High fever, jaundice, malaise are the common presenting symptoms.
Some patients can also present with a nonspecific rash, usually a purpuric morbilliform eruption.
Rarely neurologic man...
Short-term strategy: Control the hyperinflammatory state.
Long-term strategy: definitive treatment with allogeneic hematopoietic stem cell transplantation (HSCT)
Treat underlyi...
234437005 Hemophagocytic lymphohistiocytosis
724641002 Primary hemophagocytic lymphohistiocytosis
398250003 Familial hemophagocytic lymphohistio...
HLH is a rare clinical syndrome characterized by excessive activation of the immune system resulting in over production of inflammatory cytokines.
Primary HLH is usually seen in childre...
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